Table 1

Summary of the functional features of KRAB-containing zinc-finger repressor proteins

Subfamily
Protein
Species
Chromosomal localization
Number of zinc fingers
Expression pattern
Proposed function

A + B subfamily
HKr18
Human
19
20
Ubiquitous
Repressor or RNA pol II

HKr19
Human
7
11
Testis
Cell differentiation

KID-1
Human
5q35.3
13
Ubiquitous
Nucleolar integrity

Kid2
Mouse
11
13
Embryonic brain, kidney, gut and lung
Mouse development

Kid3
Mouse
11
11
Embryonic (E16.5) kidney, gut, lung and heart
Kidney development

KOX1
Human
12q24.33
9
Ubiquitous
Repressor of RNA pol I, II, and II promoters

KRAZ1
Mouse
17
15
Ubiquitous
Repressor or RNA pol II

KRAZ2
Mouse
5
9
Ubiquitous
Repressor or RNA pol II

KS1
Rat

10
Ubiquitous
Tumor suppressor

KZF-1
Rat
6
9
Testis
Spermatogenesis

RbaK
Human
7
16
Ubiquitous
Cell cycle arrest

RITA
Human
9q13
12
Ubiquitous
Thyroid carcinoma

ZBRK1
Human
19q13.41
8
Skeletal muscle
Interaction with Brca1

ZF5128
Human
19
9
Ubiquitous
T cell activation

ZNF41
Human
Xp11.2
18
Ubiquitous
Flanking a translocation breakpoint in synovial sarcoma

ZNF43
Human
19p13.1-p12
22
T cell, B cell, and Ewing cells
Differentiation and growth arrest in Ewing cells

ZNF85
Human
19p13.1-p12
15
Ubiquitous
Repressor RNA pol II

ZNF91
Human
19p12
27
Seminoma and lymphoid cells
Repression of the human Fc gamma RIIB gene

ZNF133
Human
20p11.23
15
Ubiquitous
Repressor RNA pol II

ZNF140
Human
12q24
9
Lymphoid cells
Repression of the human Fc gamma RIIB gene

ZNF141
Human
4p16.3
10
Ubiquitous
Candidate for the Wolf-Hirschhorn syndrome

ZNF157
Human
Xp11.2
12
Blood vessels
Potential hotspot for neurogenetic disorders

A subfamily
HZF12
Human
19
9
Ubiquitous
Repressor of RNA pol II

MZF31
Mouse
2
9
Ubiquitous
Repressor of RNA pol II

pMLZ-8
Mouse
4
15
Ubiquitous
Repressor of RNA pol II

ZK1
Human
19p13.2
15
Hematopoietic and various cancer cells
Radiation-induced apoptotic cell death

ZNF136
Human
19p13.1-p12
13
Ubiquitous
Weak repressor of RNA pol II

A + b subfamily
HZF4
Human
19p13.32
18
Ubiquitous
Repressor of RNA pol II

Zfp93
Human
19p13.1-p12
15
Ubiquitous
Repressor of RNA pol II

rKr2
Rat
1
19
Central nervous system and testis
Maturation of neurons and oligodendrocyte

ZNF45
Human
19p13.2
11
Ubiquitous
Potential hotspot for malignant disorders

ZNF155
Human
19q13.2
11
Ubiquitous
Repressor of RNA pol II

ZNF221
Human
19q13.2
15
Ubiquitous
Repressor of RNA pol II

ZNF222
Human
19
7
Ubiquitous
Repressor of RNA pol II

ZNF224
Human
19
16
Ubiquitous
Repressor of RNA pol II

ZNF225
Human
19
17
Ubiquitous
Repressor of RNA pol II

ZNF226
Human
19
17
Ubiquitous
Repressor of RNA pol II

SCAN subfamily
FPM315
Human
16p13.3
9
Ubiquitous
Represses the Col11a2 promoter

SKAT2
Mouse
11
14
Brain, kidney and hematopoietic cells
Regulation of cytokine in T cells

Skz1
Mouse
13
7
Ubiquitous
Repressor of RNA pol II

ZFP95
Human
7
13
Ubiquitous
Repressor of RNA pol II

ZNF197
Human
3p21.
20
Ubiquitous
Repressor of RNA pol II

ZNF202
Human
11q23.3
8
Ubiquitous
Energy metabolism

ZNF274
Human
19q
7
Ubiquitous
Repressor of RNA pol II

Urrutia Genome Biology 2003 4:231   doi:10.1186/gb-2003-4-10-231